From: Lung function monitoring in patients with duchenne muscular dystrophy on steroid therapy
FVC (L/%) | ||||
---|---|---|---|---|
Evaluation I | Evaluation II | Evaluation III | ||
Age (≤10 years) | 1.6 ± 0.3/ | 1.7 ± 0.4/ | 1.7 ± 0.4/ | p1 = 0.24/0.59 |
n = 9 | 78.8 ± 12.5 | 80.1 ± 16.6 | 75.2 ± 20.2 | p2 = 0.07/0.31 |
Age (>10 years) | 1.7 ± 0.4/ | 1.8 ± 0.4/ | 1.7 ± 0.4/ | p3 = 0.19/0.09 |
n = 12 | 66 ± 22.1 | 65.5 ± 24.7 | 60.5 ± 23.6 | |
Age of onset of steroid therapy (≤7 years) | 1.6 ± 0.3 / 75.9 ± 16.3 | 1.7 ± 0.5 / 78.5 ± 22.5 | 1.7 ± 0.4 / 74.7 ± 25.5 | p1 = 0.24/0.61 |
p2 = 0.05/0.25 | ||||
p3 = 0.21/0.23 | ||||
n = 10 | ||||
Age of onset of steroid | 1.7 ± 0.4 / 66.9 ± 21.3 | 1.8 ± 0.4 / 66.1 ± 21.7 | 1.7 ± 0.3 / 59.6 ± 18.5 | |
therapy (>7 years) | ||||
n = 11 | ||||
Ambulant | 1.7 ± 0.4 / 86.2 ± 10.6 | 1.9 ± 0.4 / 92.3 ± 11.5 | 1.9 ± 0.3 / 87.2 ± 15.6 | p1 = 0.37/0.65 |
p2 = 0.41/0.99 | ||||
n = 9 | p3 = 0.83/0.67 | |||
Non-ambulant | 1.6 ± 0.4 / 60 ± 16.3 | 1.6 ± 0.4 /56.7 ± 15.1 | 1.5 ± 0.3 / 51.5 ± 13.3 | |
n = 12 |