From: Jejunoileal atresia and cystic fibrosis: don’t miss it
Cases tested for CF | Cases not tested for CF | |
---|---|---|
(n=18) | (n=32) | |
Birth | ||
Boys | 9 (50%) | 16 (50%) |
Gestational age (weeks) | 37 (34–40) | 38 (35–39) |
Birth weight (grams) | 2518 (2180–3169) | 3020 (2300–3470) |
5 minutes Apgar score | 10 (8–10) | 10 (8–10) |
Caesarean section | 4 (22%) | 7 (22%) |
Bile stained amniotic fluid | 6 (33%) | 4 (13%) |
Prenatal ultrasound | 9 (50%) | 11 (34%) |
-polyhydramnion | 2 | 6 |
-hyperechoic bowels | 2 | 0 |
-bowel dilation | 6 | 9 |
After birth | ||
Meconium after 24 hours | 5 (28%) | 8 (25%) |
Defaecation problems later on | 3 (17%) | 8 (25%) |
Use of enema | 1 (6%) | 4 (13%) |
Sticky meconium | 1 (6%) | 0 (0%) |
Abdominal distension | 15 (83%) | 21 (66%) |
Feeding problems / vomiting | 9 (50%) | 19 (59%) |
Vomiting or aspiration of bile-stained gastric contents (nasogastric tube) | 13 (72%) | 24 (75%) |
Dilated bowels (X-ray) | 16 (89%) | 27 (84%) |
Surgery | ||
Locus of atresia | ||
-jejunal | 11 (61%) | 14 (44%) |
-ileal | 7 (39%) | 18 (56%) |
Age first surgery (days) | 2 (1–3) | 2 (1–4) |
Stomy | 3 (17%) | 4 (13%) |
Postoperative phase | ||
Aspiration of bile-stained gastric contents (nasogastric tube) 7 days or more after surgery | 10 (56%) | 8 (25%)* |
Defaecation problems | 5 (28%) | 3 (9%) |
Start enteral feeding after surgery (days) | 6 (5–9) | 4 (2–6) |
Time between start and full enteral feeding (days) | 11 (7–26) | 8 (5–10) |
Short bowel | 2 (11%) | 3 (9%) |
Complications | 14 (78%) | 11 (34%)* |
-reoperation necessary | 11 | 8 |
-infection | 10 | 8 |
-central venous line infection | 5 | 3 |
-clinical sepsis | 8 | 6 |
-pneumonia | 0 | 0 |
Ventilatory support after 7 days | 2 (11%) | 1 (3%) |
Chronic Lung Disease | 1 (6%) | 1 (3%) |
Survival | 14 (78%) | 31 (97%) |