From: Phenotypic expression of the p.Leu1077Pro CFTR mutation in Sicilian cystic fibrosis patients
Patient | FEV1 (%) | FVC (%) | SaO2(%) | Bronchiectasis | Sputum pathogens | Rhino/sinus disease | Pancreatic insufficiency | Dehydration |
---|---|---|---|---|---|---|---|---|
1 | 93.2% | 91.7% | 97% | No | S. Aureus* P. Aeruginosa** | Yes | Yes | Yes |
2 | 89.6% | 87.6% | 97% | No | S. Aureus* P. Aeruginosa** | No | Yes | No |
3 | 96% | 95% | 99% | No | S. Aureus** | No | Yes | No |
4 | 55% | 52.5% | 96% | Yes | P. Aeruginosa* | Yes | Yes | Yes |